A case of Hypomyopathic Dermatomyositis which subsequently developed to overt Myositis with ILD

Authors

  • Prayush Sharma KIST Medical College and Teaching Hospital, Imadole
  • Abhijit Datta Bangabandhu Sheikh Mujib Medical College Hospital, Faridpur, Bangladesh
  • Mohammed Zakir Hossain Cumilla Medical College Hospital, Cumilla, Bangladesh

DOI:

https://doi.org/10.3126/nrj.v1i2.54905

Keywords:

Clinically Amyopathic Dermatomyositis (CADM), Dermatomyositis (DM), Hypomyopathic Dermatomyositis (HDM), Interstitial Lung Disease (ILD), Non-specific Interstitial Pneumonia

Abstract

Dermatomyositis (DM) is an inflammatory myositis. Clinically amyopathic dermatomyositis (CADM) and hypomyopathic dermatomyositis (HDM) are rare forms of DM in which skin manifestations are present with no and minimal clinical and laboratory evidence of myositis respectively. A common complication of CADM/HDM is interstitial lung disease (ILD), with the most common histopathologic variant of non-specific interstitial pneumonia (NSIP). This case highlights the development of ILD and severe muscle weakness, including proximal limb muscles, muscles of respiration and muscles of deglutition in a patient with previous diagnosis of hypomyopathic dermatomyositis.

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Published

2022-12-31

How to Cite

Sharma, P., Datta, A., & Hossain, M. Z. (2022). A case of Hypomyopathic Dermatomyositis which subsequently developed to overt Myositis with ILD. Nepalese Respiratory Journal, 1(2), 25–27. https://doi.org/10.3126/nrj.v1i2.54905

Issue

Section

Case Reports