Dyke Davidoff Masson Syndrome with Abdominal Epilepsy-Rare Presentation

Authors

  • Shitanshu Srivastava Department of Pediatrics, Era’s Lucknow Medical College, Lucknow
  • Rajat Pratap Singh Department of Pediatrics, Era’s Lucknow Medical College, Lucknow
  • KL Srivastava Department of Pediatrics, Era’s Lucknow Medical College, Lucknow

DOI:

https://doi.org/10.3126/ajms.v3i2.6172

Keywords:

Dyke Davidoff Masson syndrome, abdominal epilepsy, cerebral hemiatrophy, mental retardation

Abstract

Dyke Davidoff Masson Syndrome (DDMS) with abdominal epilepsy, is a rare clinical condition. It is characterized by severe abdominal pain with seizures, facial asymmetry, contralateral hemiparesis, and mental retardation. Diagnosis is made clinically coupled with radiological features which include cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses along with abnormal EEG and response to antiepileptic drugs. Here we report a case of DDMS with abdominal epilepsy in a 10 year old male child who presented with recurrent episodes of severe abdominal pain followed by seizures, hemiparesis and mental retardation. CT and MRI showed hemiatrophy of right cerebral hemisphere.

DOI: http://dx.doi.org/10.3126/ajms.v3i2.6172

Asian Journal of Medical Sciences 3(2012) 25-28

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Published

2013-02-26

How to Cite

Srivastava, S., Singh, R. P., & Srivastava, K. (2013). Dyke Davidoff Masson Syndrome with Abdominal Epilepsy-Rare Presentation. Asian Journal of Medical Sciences, 3(2), 25–28. https://doi.org/10.3126/ajms.v3i2.6172

Issue

Vol. 3 No. 2 (2012)

Section

Case Reports

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