A Case of Relapsing Polychondritis with Tracheobronchial Involvement

Authors

  • Naresh Gurung Department of Pulmonary, Critical Care and Sleep Medicine, Nepal Mediciti Hospital, Bhaisepati, Lalitpur, Nepal
  • Ashish Shrestha Department of Pulmonary, Critical Care and Sleep Medicine, Nepal Mediciti Hospital, Bhaisepati, Lalitpur, Nepal
  • Ashish Karthak Department of Pulmonary, Critical Care and Sleep Medicine, Nepal Mediciti Hospital, Bhaisepati, Lalitpur, Nepal
  • Sanjeet Krishna Shrestha Department of Pulmonary, Critical Care and Sleep Medicine, Nepal Mediciti Hospital, Bhaisepati, Lalitpur, Nepal
  • Rakesh Lama Department of Pulmonary, Critical Care and Sleep Medicine, Nepal Mediciti Hospital, Bhaisepati, Lalitpur, Nepal
  • Sanjeet Bhattarai Department of Pulmonary, Critical Care and Sleep Medicine, Nepal Mediciti Hospital, Bhaisepati, Lalitpur, Nepal
  • Utsav Kumar Shrestha Department of Pulmonary, Critical Care and Sleep Medicine, Nepal Mediciti Hospital, Bhaisepati, Lalitpur, Nepal
  • Sagun khatri Department of Pulmonary, Critical Care and Sleep Medicine, Nepal Mediciti Hospital, Bhaisepati, Lalitpur, Nepal

DOI:

https://doi.org/10.3126/jaim.v11i2.52411

Keywords:

Relapsing polychondritis, tracheal stenosis, tracheobronchial chondritis, glucocorticoids

Abstract

Relapsing Polychondritis (RPC) is a rare systemic inflammatory disorder of unknown etiology and characterized by recurrent and progressive inflammation of the cartilaginous structures, particularly involving the auricles, nose and respiratory tract as well as extra-cartilaginous tissues, including eyes, heart, skin, central nervous and hematological systems. Its diagnosis can be difficult when the typical clinical features such as auricular chondritis are absent. Here, we report on a case of 43-year-old woman who presented with recurrent sore thorat, dysphagia, extertional dyspnea, cough and noisy breathing initially misdiagnosed as acute laryngitis who was eventually diagnosed as Relapsing polychondritis with tracheobronchial involvement. Chest computed tomography showed the diffuse involvement of tracheobronchial cartilage. Based on the, Damiani’s criteria, she was diagnosed as relapsing polychondritis even though there was no unique involvement of auricular cartilage, and high dose steroid and immunosuppressive therapy were then started. This case indicated that patients who have tracheobronchial cartilage involvement without definite auricular chondritis should be considered for relapsing polychondritis as a differential diagnosis. This case is reported to raise awareness of airway involvement in RPC and discuss its current management.

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Published

2023-02-12

How to Cite

Gurung, N. ., Shrestha, A. ., Karthak, A. ., Shrestha, S. K. ., Lama, R. ., Bhattarai, S. ., Shrestha, U. K., & khatri, S. . (2023). A Case of Relapsing Polychondritis with Tracheobronchial Involvement. Journal of Advances in Internal Medicine, 11(2), 55–59. https://doi.org/10.3126/jaim.v11i2.52411

Issue

Section

Case Reports