Isolated intestinal ganglioneuromatosis - A rare entity

Authors

  • Uttam Laudari Department of Pathology, Kathmandu Medical College, Kathmandu
  • Shail Rupakheti Department of Pathology, Kathmandu Medical College, Kathmandu
  • Tanka Prasad Bohara Department of Pathology, Kathmandu Medical College, Kathmandu
  • Mukunda Raj Joshi Department of Pathology, Kathmandu Medical College, Kathmandu
  • Mamta Lakhey Department of Pathology, Kathmandu Medical College, Kathmandu

DOI:

https://doi.org/10.3126/jkmc.v5i4.18612

Keywords:

Ganglioneuromatosis, Small Intestine

Abstract

Intestinal ganglioneuromatosis are rare benign tumour of ganglionic cell origin, most of them associated with neurofi bromatosis type I and multiple endocrine neoplasia type IIB. They are benign tumours with rare malignant transformation, have a varied clinical presentation and long indolent course. Surgical resection is the only modality of treatment and diagnosis is based on histopathological examination and immunohistochemistry. We report a case, 55 year old male who was diagnosed as a case of isolated intestinal ganglioneuromatosis, i.e no association with neurofibromatosis type I and multiple endocrine neoplasia type IIB. He is on regular follow up with normal daily activities and no evidence of recurrence.

Journal of Kathmandu Medical College, Vol. 5, No. 4, Issue 18, Oct.-Dec., 2016, Page: 131-135

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Author Biographies

Uttam Laudari, Department of Pathology, Kathmandu Medical College, Kathmandu

Resident

Shail Rupakheti, Department of Pathology, Kathmandu Medical College, Kathmandu

Lecturer

Tanka Prasad Bohara, Department of Pathology, Kathmandu Medical College, Kathmandu

Assistant Professor

Mukunda Raj Joshi, Department of Pathology, Kathmandu Medical College, Kathmandu

Associate Professor

Mamta Lakhey, Department of Pathology, Kathmandu Medical College, Kathmandu

Professor

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Published

2017-12-01

How to Cite

Laudari, U., Rupakheti, S., Bohara, T. P., Joshi, M. R., & Lakhey, M. (2017). Isolated intestinal ganglioneuromatosis - A rare entity. Journal of Kathmandu Medical College, 5(4), 131–135. https://doi.org/10.3126/jkmc.v5i4.18612

Issue

Section

Case Reports