Unusual Giant Syringomyelia with Neurocutaneous Melanosis

  • R Shrestha Fellow in Neurosurgery, Harvard Medical School/ Boston Children Hospital, 300 Longwood Avenue, Boston, MA 02115
  • AR Cohen Department of Neurosurgery, Harvard Medical School/Boston Children Hospital, 300 Longwood Avenue, Boston, MA 02115
Keywords: Giant Syringomyelia

Abstract

A two year old male presented with feeding intolerance and lethargy. Mother had normal delivery with term baby. The patient denied previous trauma or recent weight loss. Physical examination revealed neurocutaneous melanosis (NCM) over lower back side of body and no signs of peripheral motor deficit or abnormal reflexes. Hematological investigations showed no abnormality. Magnetic resonance (MR) imaging found a large, cystic cavity that was eccentric in the cervicothoracic spine extending from C3 to L1. Suboccipital decompressive craniectomy, bilateral C1 laminectomy, and occipital duraplasty were done.

J Nepal Paediatr Soc 2014;34(3):250-251

DOI: http://dx.doi.org/10.3126/jnps.v34i3.11165

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Abstract
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Published
2015-04-08
How to Cite
Shrestha, R., & Cohen, A. (2015). Unusual Giant Syringomyelia with Neurocutaneous Melanosis. Journal of Nepal Paediatric Society, 34(3), 250-251. https://doi.org/10.3126/jnps.v34i3.11165
Section
Images in Paediatrics