Thoracic Ectopia Cordis

  • Dipak Muktan Department of Paediatrics, BP Koirala Institute of Health Sciences (BPKIHS), Dharan
  • Rupa R Singh Department of Paediatrics, BP Koirala Institute of Health Sciences (BPKIHS), Dharan
  • Nisha Keshary Bhatta Department of Paediatrics, BP Koirala Institute of Health Sciences (BPKIHS), Dharan
Keywords: Ectopia cordis, developmental anomaly, ventral body wall developmental defects

Abstract

Ectopia Cordis is a rare congenital anomaly characterized by partial or complete displacement of the heart outside the thoracic cavity with an estimated incidence of 5 to 8 per million live births We report a case of a 22-year-old primigravida, unbooked and immunized woman, with no relevant family or personal history, in which the prenatal fetal ultrasound, performed at 34 weeks of gestation, revealed a defect of the anterior chest wall with exteriorization of the heart. Baby was Pre-term 34 week by date but term by modified Ballard scoring, male weighing 2.4 kg delivered by lower segment caesarean section. Baby had complete thoracic ectopia cordis with large defect in anterior wall of chest and sternum was absent.

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Author Biographies

Dipak Muktan, Department of Paediatrics, BP Koirala Institute of Health Sciences (BPKIHS), Dharan
Senior Resident
Rupa R Singh, Department of Paediatrics, BP Koirala Institute of Health Sciences (BPKIHS), Dharan
Professor
Nisha Keshary Bhatta, Department of Paediatrics, BP Koirala Institute of Health Sciences (BPKIHS), Dharan
Professor
Published
2018-06-07
How to Cite
Muktan, D., Singh, R., & Bhatta, N. (2018). Thoracic Ectopia Cordis. Journal of Nepal Paediatric Society, 37(3), 293-295. https://doi.org/10.3126/jnps.v37i3.18662
Section
Case Reports