Disappearing Bone Disease with Disappearing Spleen!
Keywords:Gorham's disease (disappearing bone disease), osteolytic lesions, spleen
A 6-year-old girl who reported for pain abdomen was incidentally detected to have multiple osteolytic lesions on X-ray. She was diagnosed as a case of Gorham's disease following confirmation with histopathology and kept on close follow-up. She was admitted again after 2 years for fever and investigations revealed an absent spleen apart from multicentric osteolytic lesions. This is the first case reported of a child with Gorham's disease who has had an auto-splenectomy on follow-up.
Key words: Gorham's disease (disappearing bone disease), osteolytic lesions, spleen.
J. Nepal Paediatr. Soc. Vol 29, No. 2, pp.94-97
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