Disappearing Bone Disease with Disappearing Spleen!

Authors

  • BM John Classified Specialist (Pediatrics), Department of Pediatrics. Command Hospital (Air Force), Bangalore
  • Daljit Singh Professor and Head of Department of Pediatrics. Command Hospital (Air Force), Bangalore

DOI:

https://doi.org/10.3126/jnps.v29i2.2047

Keywords:

Gorham's disease (disappearing bone disease), osteolytic lesions, spleen

Abstract

A 6-year-old girl who reported for pain abdomen was incidentally detected to have multiple osteolytic lesions on X-ray. She was diagnosed as a case of Gorham's disease following confirmation with histopathology and kept on close follow-up. She was admitted again after 2 years for fever and investigations revealed an absent spleen apart from multicentric osteolytic lesions. This is the first case reported of a child with Gorham's disease who has had an auto-splenectomy on follow-up.

Key words: Gorham's disease (disappearing bone disease), osteolytic lesions, spleen.  

doi: 10.3126/jnps.v29i2.2047

J. Nepal Paediatr. Soc. Vol 29, No. 2, pp.94-97

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Published

2009-07-16

How to Cite

John, B., & Singh, D. (2009). Disappearing Bone Disease with Disappearing Spleen!. Journal of Nepal Paediatric Society, 29(2), 94–97. https://doi.org/10.3126/jnps.v29i2.2047

Issue

Section

Brief Reports/Case Reports/Case Series