Holocord Syrinx, Tethered Cord and Diastematomyelia: Case Report and Review of Literature

  • A Maheshwari Assistant Professor, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
  • D Yadav Senior Resident, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
  • S Aneja Director Professor, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
  • S Kaur Senior Resident, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
  • B Patra Senior Pediatrician, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
  • A Seth
Keywords: Tethered cord, Holocord syrinx, Diastematomyelia

Abstract

Syringomyelia refers to the presence of cavities within the spinal cord or a dilatation of the central spinal cord canal. In 90% of cases, syringomyelia is associated with a Chiari I malformation. The association of syringomyelia with tethered cord is well known but syrinxes associated with these defects are usually below vertebral level T6. Holocord syrinx associated with tethered cord is rare and is almost always associated with Chiari 1 malformation. To the best of our knowledge, only a single case report of holocord syrinx with tethered cord has been reported, but this patient had multiple overt lumbosacral defects (tethered cord, meningocele and diastematomyelia). We are reporting a three year old child with holocord syrinx with tethered cord and diastematomyelia and no evidence of Chiari malformation, meningocele or any overt spinal malformation and minimal neurological abnormalities.

J Nepal Paediatr Soc 2012;32(2):169-171

doi: http://dx.doi.org/10.3126/jnps.v32i2.6098

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Author Biography

S Kaur, Senior Resident, Department of Paediatrics, Lady Hardinge Medical College, New Delhi
Pediatrics, Lady Hardinge Medical College, New Delhi
Published
2012-10-01
How to Cite
Maheshwari, A., Yadav, D., Aneja, S., Kaur, S., Patra, B., & Seth, A. (2012). Holocord Syrinx, Tethered Cord and Diastematomyelia: Case Report and Review of Literature. Journal of Nepal Paediatric Society, 32(2), 169-171. https://doi.org/10.3126/jnps.v32i2.6098
Section
Brief Reports/Case Reports/Case Series