Phthisis Bulbi and Leptomeningeal Metastasis in a Case of Trilateral Retinoblastoma
DOI:
https://doi.org/10.3126/njr.v3i2.9621Keywords:
Leptomeningeal metastasis, Phthisis bulbi, Pineoblastoma, PNET, Trilateral retinoblastomaAbstract
Retinoblastoma (RB) is the most common ocular malignant neoplasm of childhood. Bilateral or unilateral intraocular RB in conjunction with a primitive neuroectodermal tumor (PNET) of the pineal region (i.e. pineoblastoma) is termed as trilateral retinoblastoma (TRB). Retinoblastoma may spread along the optic nerve to the intracranial compartment to give drop metastases in the subarachnoid space or it can spread through hematogenous and lymphatic routes. Phthisis bulbi (PB) is a relatively uncommon presentation of retinoblastoma. We report a case of trilateral retinoblastoma with phthisical left eye and extensive leptomeningeal metastasis in a 3-year-old female child.
DOI: http://dx.doi.org/10.3126/njr.v3i2.9621
Nepalese Journal of Radiology Vol.3(2)July-Dec, 2013: 92-96
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