Abernethy Malformation and the Spectrum of Imaging Findings: A Case Report

Authors

  • K Gangadhar Department of Body Imaging and Intervention, UTHSCSA, San Antonio
  • SV Nair Department of Body Imaging and Intervention, UTHSCSA, San Antonio
  • A Sunnapwar Department of Body Imaging and Intervention, UTHSCSA, San Antonio
  • KN Chintapalli Department of Body Imaging and Intervention, UTHSCSA, San Antonio

DOI:

https://doi.org/10.3126/njr.v3i2.9622

Keywords:

Abernethy malformation, congenital extrahepatic porto systemic shunt, Congenital portosystemic shunts, Nodular regenerative hyperplasia, Skeletal anomalies

Abstract

Congenital extrahepatic porto systemic shunt (CEPS) is a rare condition in which the porto mesenteric blood drains into a systemic vein, bypassing the liver through a complete or partial shunt. It is commonly associated with multiple congenital anomalies. A diagnosis of Abernethy malformation is made by non-invasive cross-sectional imaging techniques such as Doppler ultrasound, CT or MRI, which show the shunt and intrahepatic portal vein branches. We report a case presenting with psychological issues, systemic hypertension, upper extremity deformities, liver lesions and portal hypertension. Usually the patients are diagnosed in childhood, in our case the patient is a middle aged woman. This case report shows the importance of imaging in diagnosis of this condition and presentation of the patient with portal hypertension which is rare.

DOI: http://dx.doi.org/10.3126/njr.v3i2.9622

Nepalese Journal of Radiology Vol.3(2)July-Dec, 2013: 97-102

 

 

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Published

2014-01-16

How to Cite

Gangadhar, K., Nair, S., Sunnapwar, A., & Chintapalli, K. (2014). Abernethy Malformation and the Spectrum of Imaging Findings: A Case Report. Nepalese Journal of Radiology, 3(2), 97–102. https://doi.org/10.3126/njr.v3i2.9622

Issue

Section

Case Reports