Moyamoya Disease with Intraventricular Hemorrhage in a Child: A Case Report

Authors

  • Nisha Regmi College of Medical Sciences, Chitwan, Nepal
  • Bibek Shrestha Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, Nepal
  • Vivek Karn Department of Pediatrics, Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, Nepal
  • Pradeep Raj Regmi Department of Radiology, Maharajgunj Medical Campus, Tribhuvan University Teaching Hospital, Institute of Medicine, Kathmandu, Nepal

Keywords:

Moyamoya disease, intraventricular hemorrhage, pediatric stroke

Abstract

Moyamoya disease is a rare progressive cerebrovascular disorder in Nepal characterized by stenosis or occlusion of cerebral arteries with abnormal collateral vessels, and hemorrhagic presentation in children is extremely uncommon. We report an 8-year-old girl with intraventricular hemorrhage presenting with seizures, vomiting, and decreased consciousness. Imaging revealed characteristic angiographic features of Moyamoya disease. She was managed with external ventricular drainage and supportive treatment, achieving significant recovery. This case highlights the importance of considering Moyamoya disease in pediatric hemorrhagic stroke and underscores the need for early imaging and timely intervention.

 

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Published

2025-08-31

How to Cite

Regmi, N., Shrestha, B., Karn, V., & Regmi, P. R. (2025). Moyamoya Disease with Intraventricular Hemorrhage in a Child: A Case Report. Journal of Institute of Medicine Nepal, 47(2), 103–106. Retrieved from https://www.nepjol.info/index.php/JIOM/article/view/88892

Issue

Vol. 47 No. 2 (2025): Journal of Institute of Medicine Nepal

Section

Case Reports

License

Copyright (c) 2026 The Author(s)

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