Complete Androgen Insensitivity Syndrome with Sertoli Cell Adenoma: A Case Report and Review of Literature

Authors

  • P Sharma Department of Radiology, Manipal Teaching Hospital, Pokhara
  • B Karki Department of Surgery, Nepalgunj Medical College Teaching Hospital, Banke
  • S Gupta Department of Surgery, Nepalgunj Medical College Teaching Hospital, Banke
  • NM Shrestha Department of Surgery, Nepalgunj Medical College Teaching Hospital, Banke
  • P Gautam Ghimire Department of Pathology, Nepalgunj Medical College Teaching Hospital, Banke
  • RG Goel Department of Pathology, Nepalgunj Medical College Teaching Hospital, Banke

DOI:

https://doi.org/10.3126/njr.v1i1.6327

Keywords:

Complete androgen insensitivity syndrome, Sertoli cell adenoma, Primary amenorrhoea

Abstract

Complete androgen insensitivity syndrome is a rare X-linked recessive disorder. In patients with this syndrome, testicular tumors, especially seminoma, may develop after puberty. Gonadal malignancies like sertoli cell tumor, yolk sac tumor; embryonic teratoma and unclassified sex cord stromal tumor are rare in these patients. We present here, a case of complete androgen insensitivity syndrome with sertoli cell adenoma in a 25 years old patient who presented to us with history of primary amenorrhoea and bilateral inguinal swellings and was managed with bilateral gonadectomy.

DOI: http://dx.doi.org/10.3126/njr.v1i1.6327

Nepalese Journal of Radiology Vol.1(1): 61-64

 

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Published

2012-06-16

How to Cite

Sharma, P., Karki, B., Gupta, S., Shrestha, N., Ghimire, P. G., & Goel, R. (2012). Complete Androgen Insensitivity Syndrome with Sertoli Cell Adenoma: A Case Report and Review of Literature. Nepalese Journal of Radiology, 1(1), 61–64. https://doi.org/10.3126/njr.v1i1.6327

Issue

Section

Review Article